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Autosomal Dominant Polycystic Kidney Disease: A Case Report and Application of Neuman Nursing Theory

Chetan Ramesh Sangati, Somshekar Kodliwad

Abstract


Autosomal dominant polycystic kidney disease is abbreviated as ADPKD which is one of the most common, life-threatening genetic diseases which is characterized by fluid-filled cysts develop and enlarge in both kidneys result in kidney failure.  Autosomal dominant polycystic kidney disease is result of mutations in the PKD1 and PKD2 gene. ADPKD is the fourth leading cause of kidney failure. In this condition more than 50 percent of people suffered with ADPKD and it results in develop kidney failure by age 50 and is a painful disease that impacts will be every worst on quality of life.  The average size of an affected kidney is a human fist. Polycystic kidneys can grow as large as a football, and weighing up to 30 pounds each. The most common symptoms are pain in the back and the sides and headaches. Other symptoms include liver and pancreatic cysts, urinary tract infections, abnormal heart valves, high blood pressure, kidney stones, brain aneurysms, and diverticulitis.  Dialysis or kidney transplant is the only options to treat ADPKD.


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